Hamartoma mesenquimal hepático: relato de dois casos de tumor hepático benigno na infância

Abstract

INTRODUCTION: Hepatic mesenchymal hamartoma is a benign tumor more common in children. Comprised of fibrous tissue and with a variable amount of blood vessels and bile ducts, it is asymptomatic in most cases but abdominal distention and pain on palpation can be reported. CASES REPORT: Two infants with large abdominal mass and imaging studies showing cystic hepatic lesions with septations in its interior, suggestive of hepatic mesenchymal hamartoma. One of the patients underwent surgical resection and the other living-donor liver transplantation. Both are deemed healed and currently asymptomatic. CONCLUSIONS: Hepatic mesenchymal hamartoma should be suspected whenever a child younger than 5 years, especially before 2 years of age, presents itself with increased abdominal volume. Even though both patients had the same diagnosis, their treatment strategies were different to eradicate the tumor. When treating a large tumor, the surgical planning must include the possibility of a living-donor transplantation during the procedure.