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Tipo:	Artigo de Periódico
Título:	Jejunal stromal tumor and neurofibromatosis
Autor(es):	Daniela Fonseca Lisboakayser Lígia Nascimento Figueiredo Amaral Livia Paulucci Cavalcanti Andrade Fernando Augusto Santos Vasconcelos Luiz Felipe de Campos-lobato Juliano Alves Figueiredo
Resumen:	Gastrointestinal stromal tumors, although rare, are the most common primary mesenchy mal neoplasms of the gastrointestinal tract and originate from the interstitial cells of Cajal.They present slow growth and symptoms such as bleeding, abdominal pain or discomfort,and the presence of an abdominal mass. The most affected organs are the stomach and small intestine. Differential diagnoses for gastrointestinal stromal tumor include adenocar cinoma and small intestine lymphoma, metastasis, and carcinoid tumor. Gastrointestinal stromal tumors have been associated with familial syndromes such as type 1 neurofibro matosis, considered a predisposing factor for tumors in the small intestine. This study aimed to report a case of gastrointestinal stromal tumor in the jejunal region in a patient with type 1 neurofibromatosis, followed-up for two years, who underwent laparoscopic segmental enterectomy and diagnosis determined by histopathology and immunohistochemistry. The diagnosis of small intestine gastrointestinal stromal tumor is challenging because of its low incidence, nonspecific symptoms, relative inaccessibility of the small intestine to conventional endoscopic examination, broad spectrum of radiological appearances, and the fact that the nature of the mass is difficult to determine with imaging examinations of the abdomen alone. Thus, the small intestine gastrointestinal stromal tumor may be erroneously diagnosed as pancreatic, gynecological, or mesenteric tumors. The literature does not present many reports on the association of jejunal gastrointestinal stromal tumor with neurofibromatosis. Understanding the tumoral behavior of small intestine gastrointestinal stromal tumor in this subgroup of patients would allow better follow-up.
Asunto:	Neoplasias Gastrointestinais Tumores do Estroma Gastrointestinal Intestino Delgado Neurofibromatose 1
Idioma:	eng
País:	Brasil
Editor:	Universidade Federal de Minas Gerais
Sigla da Institución:	UFMG
Departamento:	MED - DEPARTAMENTO DE CIRURGIA
Tipo de acceso:	Acesso Aberto
Identificador DOI:	10.1016/j.jcol.2019.05.006
URI:	http://hdl.handle.net/1843/57860
Fecha del documento:	2019
metadata.dc.url.externa:	https://www.thieme-connect.de/products/ejournals/abstract/10.1016/j.jcol.2019.05.006
metadata.dc.relation.ispartof:	Journal of Coloproctology
Aparece en las colecciones:	Artigo de Periódico

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